P00439 PH4H_HUMAN
Gene name: PAH
Protein name: Phenylalanine-4-hydroxylase (PAH) (EC

List of molecules and drugs that interact with protein P00439

# DrugDomain Data PBD ligand DrugBank Accession PubChem ChEMBL Name Drug action Affinity data
1 P00439_3QI 3QI n/a 2816621 n/a 5,6-DIMETHYL-3-(4-METHYL-2-PYRIDINYL)-2-THIOXO-2,3-DIHYDROTHIENO[2,3- D]PYRIMIDIN-4(1H)-ONE n/a
2 P00439_CL CL n/a 312 n/a CHLORIDE ION n/a
3 P00439_DAH DAH DB01235 6047;6971033; CHEMBL1009 3,4-DIHYDROXYPHENYLALANINE n/a
4 P00439_FE FE n/a 29936 n/a FE (III) ION n/a
5 P00439_FE2 FE2 n/a 27284 n/a FE (II) ION n/a
6 P00439_H2B H2B DB02562 133246;135398653; n/a 2-AMINO-6-(1,2-DIHYDROXY-PROPYL)-7,8-DIHYDRO-6H-PTERIDIN-4-ONE n/a
7 P00439_H4B H4B DB00360 44257;5282445;135398654; CHEMBL1201774 5,6,7,8-TETRAHYDROBIOPTERIN cofactor
8 P00439_HBI HBI DB04400 119055;5288515;135398687; n/a 7,8-DIHYDROBIOPTERIN n/a
9 P00439_LDP LDP DB00988 681 CHEMBL59 L-DOPAMINE n/a
10 P00439_LNR LNR DB00368 439260 CHEMBL1437 L-NOREPINEPHRINE inhibitor
11 P00439_NLE NLE DB15458 21236;6991974; CHEMBL292439 NORLEUCINE n/a
12 P00439_PHE PHE DB00120 6140;6925665; CHEMBL301523 PHENYLALANINE n/a
13 P00439_SO4 SO4 DB14546 1117 n/a SULFATE ION n/a
14 P00439_TIH TIH DB03673 146719;7111748; CHEMBL1236302 BETA(2-THIENYL)ALANINE n/a
15 P00439_XDE XDE n/a 247704 CHEMBL42280 4-[(1S)-1-hydroxy-2-(methylamino)ethyl]benzene-1,2-diol n/a
16 P00439_DB00120 n/a DB00120 n/a n/a Phenylalanine n/a
17 P00439_DNE DNE DB04419 n/a n/a D-norleucine n/a
18 P00439_DB06262 n/a DB06262 n/a n/a Droxidopa inhibitor